Hypoplastic left-heart syndrome.

Hypoplastic left heart syndrome: parent support for early decision making.

Hypoplastic left heart syndrome is a life threatening congenital cardiac anomaly. After a child has been diagnosed with hypoplastic left heart syndrome, parents must make life or death decisions within days of birth. Healthcare providers must provide appropriate education so that parents are able to make informed, timely decisions. Information regarding the diagnosis, treatment options, and par...

The myocardial and coronary histopathology and pathogenesis of hypoplastic left heart syndrome.

Hypoplastic left heart syndrome has the greatest mortality rate among all CHDs and without palliation is uniformly fatal. Despite noble efforts, the aetiology of this syndrome is unknown and a cure remains elusive. The genetic and anatomic heterogeneity of hypoplastic left heart syndrome supports a rethinking of old hypotheses and warrants further investigation into the histological and vascula...

Hypoplastic left heart syndrome and 45X karyotype.

A review of 63 patients with 45X karyotype (Turner's syndrome) admitted to a hospital from 1972 to 1985 showed that 20 (32%) had one or more major cardiac malformations (mostly coarctation and aortic stenosis). Four (20%) died in the neonatal. One infant had mitral stenosis and severe aortic stenosis and died at the age of 35 days. The three (15%) other patients who died had a typical hypoplast...

Hypoplastic left heart syndrome with right aortic arch in a newborn.

A patient with the rare combination of a right-sided aortic arch in hypoplastic left heart syndrome with an incomplete vascular ring is described.

Beyond Hypoplastic Left Heart Syndrome: The Spectrum of Congenital Heart Disease Associated with Left Ventricular Hypoplasia

Left ventricular hypoplasia complicates other forms of congenital heart disease in addition to the classic ‘‘hypoplastic left heart syndrome.’’ Within this heterogeneous group, subtle anatomic differences determine surgical management and ultimate prognosis. Thus, an individualized approach is necessary to optimize outcomes in this complex population.

Right ventricular resynchronization in a child with hypoplastic left heart syndrome.